A
Acidemia, methylmalonic 204
Adrenocorticotropic hormone 110
Adult familial myoclonic epilepsy, benign 154
Aicardi syndrome 107
Alpers disease 204
Alpers syndrome 127
Amaurosis 76
Amygdalohippocampectomy 19
Anesthesia, general 214
Anoxia 185
Aphasia, transient 176
Arteriovenous malformations 223
Astrocytic tumors, low grade 219
Ataxia 176
Autosomal dominant
cortical myoclonus 154
epilepsy 273
familial focal epilepsy syndromes 166
inheritance 158
Azathioprine 178
C
Cannabidiol 199
Cardiac rhythm disorders 4
Cardiomyopathy 120
Carnitine deficiency 204
Cataplexy 155
Catastrophic status epilepticus, acute 128
Caudate atrophy 243f
Cavernous angiomas 222
Cerebrovascular disease 90
Chemoradiotherapy 238f
Childhood epilepsy, benign 63
Chromosomal syndromes 90
Cingulate gyrus 4
Clonic seizures 86
Corpus callosum, agenesis of 107
Cortical synaptogenesis, period of 145
Creatine defect disorders 111
Creutzfeldt-Jakob disease 177
Cyclophosphamide 178
D
Déjà vu phenomenon 169
Dentato-rubral-pallidoluysian atrophy 159
Digital subtraction angiography 224
Diplopia 198
Disseminated encephalomyelitis, acute 173
Dorsal thalamic nucleus 145
Dorsolateral cortex 4
Down syndrome 140
Drop attacks 155
Dysconjugate eye movements 111
Dyselectrolytemias 90
Dyskinesia, paroxysmal exercise-induced 177
Dyspnea 4
E
atypical benign partial 71
Euphoria 17
European Stroke Organization 186
Eye closure 39
F
Fluorodeoxyglucose-positron emission tomography 252
Folinic acid 116
G
Ganglia encephalitis, basal 174
Gastroenteritis 182
Gaucher's disease 159
Gene test 158
Gliotic sequelae 236
Glucose transporter 127
Glutamatergic neurons 145
Glutamic acid decarboxylase 174
Glycine encephalopathy 127
Gustatory 267
H
Haemophilus influenzae 183
Hashimoto's encephalopathy 176
Head-retraction reflex 156
Hematoma, parenchymal 186
Hemifacial jerks 76
Hemispheric epilepsy surgery 253
Hemispherotomy 253
Hodgkin's lymphoma 174
Hot water epilepsy 38
Hydrocephalic attack 155
Hyperglycinemia, non-ketotic 112
Hyperintense rim, peripheral 226f
Hyperthermia 134
Hyperventilation 56
Hypocalcemia 204
Hypoglycemia 56
Hypometabolism 146
Hypoperfusion 147
Hypothesis generation 7
I
Ictal hemianopia 17
Infantile
Intracarotid sodium amytal test 252
Intracranial
Intranasal midazolam 206
Intrauterine infections 90t
L
Leigh disease 204
Lesionectomy 238f
Lethargy, complex syndrome of 176
Leukoencephalitis 173
Lorazepam 206
Lymphoblastic leukemia, acute 238f
M
Macular cherry-red spot 158
Magnetoencephalogram 148f
Malignant migrating partial seizures 113
Mammillary bodies, agenesis of 107
Maple syrup urine disease 111
Meningoencephalitis 236
Mental retardation 134
Metabolic disease 108
Migraine 28t
Mitochondrial disorders 204
Molybdenum cofactor deficiency 127
Motor seizures 64
Movement disorder 176
Multiple independent spike foci 139
Mycophenolate mofetil 178
Myelitis 177
N
N-acetylaspartate 215
Neurocutaneous syndromes 239
Neurocysticercosis 185
Neuronal surface antibody syndrome 179
Nodular heterotopias 30f
Nystagmus 28
P
Palpitations 5
Parasaggital parieto-occipitalpolymicrogyria, bilateral 30f
Parietal operculum 17
Parieto-temporo-occipital junction 17f
Partial motor seizures 146
Pediatric
status epilepticus 204t
temporal lobe epilepsy 17t
Perinatal
Photosensitive epilepsy 40
Plasma exchange 179
Plasmapheresis 178
Pleomorphic xanthoastrocytoma 222
Polioencephalitis 173
Pontomedullary reticular formation 141
Postencephalitis 250
Posthemispherotomy status 242f
Psychogenic non-epileptic seizures 155
Psychomotor retardation, severe 108
Psychosis 175
Pulse intravenous methylprednisolone 178t
Putaminal hyperintensity 243f
Pyogenic meningitis 182
Pyridoxine 116
R
Randomized controlled trials 198
types of 39t
refractory 254fc
Refractory posterior cortex epilepsy 34f
Renin angiotensin system 73
Respiratory tract infections 182
Reticular thalamic neurons 73
S
Saxitoxin binding protein 107
Sebaceous nevus syndrome 107
Sedation 214
acute 134
concomitant non-febrile 133
eating induced 48
electroencephalographic 87
freedom 20
frequency of 64
hemiclonic 164
partial 267
post-stroke 186
post-traumatic 185
semiology 26
startle induced 49
susceptibility syndromes, benign 63
types 163
Sialidosis 159
Sialo-oligosaccharides 158
Single photon emission computed tomography 141
Skin biopsy 158
Spatial statistics, tract-based 215
Spike-wave index 73
Static encephalopathy 155
Steroids 251
Streptococcus pneumoniae 183
Stress, post-traumatic 185
Sulfite oxidase 112
Sunflower syndrome 47
Syncope 155
T
Tachycardia 5
Tay-Sachs disease 159
Temporo-parieto-occipital malformation 33f
Thermoregulation disorders 4
Thromobocytopenia 207
Todd's palsy 17
Transmantle hyperintensity 233
Truncal hypotonia 111