We present a case of 40-year-old male who presented with backache, numbness and gradually progressive weakness of lower limbs of 6 months duration. Magnetic resonance imaging (MRI) revealed a homogeneously enhancing tumor in the conus with holocord syrinx suggestive of a hemangioblastoma. Hemangioblastoma of the conus medullaris is a rare pathology especially when it is not associated with vHL syndrome. Here we discuss surgical nuances of operating upon such a rare pathology and briefly review the literature.