Cardiac rhabdomyoma is the most common benign pediatric cardiac tumor.¹ Frequently, they are associated with tuberous sclerosis, an autosomal disorder resulting in hamartomatous lesions inside the brain, heart, lungs, and kidneys. Bidirectional Glenn (BDG) shunt is a type of palliative procedure done in infants and the pediatric age group, which drains blood from the superior vena cava (SVC) into the pulmonary circulation, especially in univentricular physiology,² to improve oxygenation. Here, we present an interesting case of an acyanotic pediatric patient presenting with a right ventricular (RV) tumor, in which the BDG was performed to offload the RV, which was not reported previously in the literature. Written consent for the publication of this case was obtained from the patient\'s relatives. Also, the authors were directly involved in the perioperative care of the patient.