Xeroderma Pigmentosa is caused by an autosomal recessive allele. It is characterized by dry, pigmented skin, spidery blood vessels in the skin, skin cancers, and sometimes other abnormalities of both the eyes and brain. A harsh reaction to sunlight, such as severe sunburn and blistering at only a slight exposure, is a notable symptom and should be distinguished within the first year or two of life. The majority of the people who are born with these disorders die by early adulthood due to malignant cancers. This article reports a case of 6-year-old child suffering from XP with dental implications.