Background: Tumors of salivary glands are rare and constitute only 3% of all head and neck tumors. Pleomorphic adenoma is the most common tumor of the salivary glands. The most common salivary gland to be involved in the parotid gland. Pleomorphic adenoma of the submandibular and sublingual salivary glands is uncommon. Case report: A 14-year-old boy presented with a history of swelling in the left submandibular region for two years, slow-growing & painless in nature. On examination there was a spherical swelling measuring 4×3 cm in the left submandibular region, non-tender, firm, mobile & Bi-manually palpable. Conclusion: Pleomorphic adenoma can be a dilemma to diagnose and treat. Imaging studies with MRI and ultrasonography may be helpful in diagnosis. Total excision of the tumor and gland is recommended treatment.