Giant Thoracocervical Lymphangioma with Multivisceral Involvement: A Different Concept

JOURNAL TITLE: International Journal of Phonosurgery & Laryngology

Author
1. G Raghavendra Prasad
2. Madhavi Nori
3. MD Naseeruddin
4. JV Subba Rao
5. SS Quadri
ISSN
2230-7508
DOI
10.5005/jp-journals-10023-1085
Volume
4
Issue
2
Publishing Year
2014
Pages
4
Author Affiliations
    1. Department of Pediatric Surgery, Deccan College of Medical Sciences, Hyderabad, Telangana, India
    1. Department of Radiology, Deccan College of Medical Sciences, Hyderabad, Telangana, India
    1. Department of Radiology, Deccan College of Medical Sciences, Hyderabad, Telangana, India
    1. Department of Anesthesia, Deccan College of Medical Sciences, Hyderabad, Telangana, India
    1. Department of Pathology, Deccan College of Medical Sciences, Hyderabad, Telangana, India
  • Article keywords

    Abstract

    Background

    Lymphangiomas are benign lymphatic malformations frequently seen in head and neck region. Most reported cases are cervical lesions with mediastinal extension.1,2

    Most are conceived as due to failure of fetal lymph sacs. Synchronous or metachronus lymphangiomatosis with cystic hygroma of the neck is also reported.3

    Case details

    Massive multicompartmental mediastinal lymphangioma with cervical extension and concomitant visceral involvement is presented. It is proposed as a hamartomatous tumor rather than malunion of fetal jugular lymphatic sacs.2 Solid intrathoracic component with cystic neck extension supports mediastinal origin. Cell culture lines at 4 months were positive for endothelial cell lines positive for factor VIII antigen.

    Conclusion

    Giant thoracocervical lymphangioma is more likely to be a tumor rather than simple fetal failure of lymphatic sac fusion. Surgical excision is curative.

    How to cite this article

    Prasad GR, Nori M, Naseeruddin MD Rao JVS, Quadri SS. Giant Thoracocervical Lymphangioma with Multivisceral Involvement: A Different Concept. Int J Phonosurg Laryngol 2014;4(2):63-66.

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