The orbit is involved in 10% of all lymphomas. Paranasal sinuses and nose are other sites for extranodal lymphoma that are involved in upto 2.6 to 6.7% of lymphomas involving head and neck region and are second most common presentation of extranodal lymphoma. In nearly 22.5% of patients, sinonasal lymphoma and orbital lymphoma may coexist. The present report describes such patient with first presentation to an ophthalmologist with an attempt to review the present literature of coexistent orbital and paranasal sinuses lymphoma.